Palliative care in patients with cystic fibrosis: A systematic review
Keywords:
Palliative care, cystic fibrosis, quality of life, psychosocial supportAbstract
Palliative care consists of supportive treatments focused on terminally ill patients and their families. Therefore, the objective of this systematic review was to analyze the role of palliative care in patients with cystic fibrosis through a systematic review to identify approaches, intervention strategies, and benefits. The methodology was based on a systematic review using the PRISMA method, consulting the SciELO, Redalyc, PubMed, Scopus, and Dialnet databases, which allowed for the selection of 12 studies in English and Spanish between 2020 and 2025. The results revealed that the approaches applied in palliative care comprehensively addressed the physical, social, emotional, and spiritual dimensions, together with advance planning and interviews to recognize patients' symptoms; the strategies used in the application of palliative care during routine care included the use of validated tools such as IPOS, emotional and psychosocial support through groups, pharmacological management, counseling, and therapies; the reported benefits included early detection of needs, reduction of pain, fatigue, and stress, emotional well-being, as well as empowerment in decision-making for both patients and family members, improving quality of life.
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Copyright (c) 2025 Alexandra Maribel Salcán-Lemache, Carmen Victoria Molina-Calle, Diego Raúl Bonifaz-Díaz
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